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ICD-10 Coding for Congenital Hypothyroidism(E03.1, E03.0)

Complete ICD-10-CM coding and documentation guide for Congenital Hypothyroidism. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

CHNeonatal Hypothyroidism

Related ICD-10 Code Ranges

Complete code families applicable to Congenital Hypothyroidism

E03.0-E03.1Primary Range

Congenital hypothyroidism with or without goiter

These codes cover congenital hypothyroidism, distinguishing between cases with and without goiter.

Postprocedural hypothyroidism

Used for hypothyroidism resulting from medical procedures, relevant for differential diagnosis.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
E03.1Congenital hypothyroidism without goiterUse when congenital hypothyroidism is confirmed without goiter.
  • TSH >40 mIU/L
  • Free T4 <10 IU/L
  • Thyroid ultrasound showing ectopic or absent gland
E03.0Congenital hypothyroidism with diffuse goiterUse when congenital hypothyroidism is confirmed with goiter.
  • Palpable thyroid enlargement
  • Elevated thyroglobulin levels

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for congenital hypothyroidism

Essential facts and insights about Congenital Hypothyroidism

The ICD-10 code for congenital hypothyroidism without goiter is E03.1, and with goiter is E03.0.

Primary ICD-10-CM Codes for congenital hypothyroidism

Congenital hypothyroidism without goiter
Billable Code

Decision Criteria

clinical Criteria

  • Confirmed congenital hypothyroidism without goiter.

Applicable To

  • Congenital hypothyroidism without thyroid enlargement

Excludes

  • Transient neonatal hypothyroidism

Clinical Validation Requirements

  • TSH >40 mIU/L
  • Free T4 <10 IU/L
  • Thyroid ultrasound showing ectopic or absent gland

Code-Specific Risks

  • Incorrectly coding as E03.9 when specific criteria are met for E03.1.

Coding Notes

  • Ensure lab results and imaging are documented to support diagnosis.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Family history of endocrine/metabolic disorders

Z83.3
Use when there is a documented family history of thyroid disorders.

Encounter for routine child health exam with abnormal findings

Z00.110
Use for follow-up visits after initial screening.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Other specified hypothyroidism

E03.8
Use for transient neonatal hypothyroidism that resolves by 3 months.

Hypothyroidism, unspecified

E03.9
Avoid use unless etiology is truly unknown.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Congenital Hypothyroidism to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code E03.1.

Impact

Clinical: May lead to inappropriate treatment., Regulatory: Fails to meet coding standards., Financial: Could result in claim denials.

Mitigation Strategy

Ensure detailed lab and imaging documentation., Use specific ICD-10 codes.

Impact

Reimbursement: Potential denial of claims due to lack of specificity., Compliance: Non-compliance with coding guidelines., Data Quality: Inaccurate data affecting patient records.

Mitigation Strategy

Use E03.1 or E03.0 when specific criteria are met.

Impact

Risk of using unspecified codes when specific codes are applicable.

Mitigation Strategy

Educate coders on specific criteria for congenital hypothyroidism.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Congenital Hypothyroidism, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Congenital Hypothyroidism

Use these documentation templates to ensure complete and accurate documentation for Congenital Hypothyroidism. These templates include all required elements for proper coding and billing.

Newborn with confirmed congenital hypothyroidism

Specialty: Pediatrics

Required Elements

  • Maternal history
  • Physical exam findings
  • Lab results
  • Imaging results
  • Diagnosis statement

Example Documentation

Neonate presents with elevated TSH (55 mIU/L). Confirmatory labs: TSH 58 mIU/L, free T4 0.6 ng/dL. Thyroid scan: absent uptake. Diagnosis: congenital hypothyroidism without goiter (E03.1).

Examples: Poor vs. Good Documentation

Poor Documentation Example
Baby has hypothyroidism. Start levothyroxine.
Good Documentation Example
Neonate (3 days old) with elevated newborn screen TSH (55 mIU/L). Confirmatory venous TSH 58 mIU/L, free T4 0.6 ng/dL. Thyroid scan: absent uptake. Diagnosis: congenital hypothyroidism without goiter (E03.1).
Explanation
The good example provides specific lab values and imaging results, supporting the diagnosis.

Need help with ICD-10 coding for Congenital Hypothyroidism? Ask your questions below.

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