ICD-10 Coding for Crigler-Najjar Syndrome with Vasculitis(E80.5, L95.9)
Complete ICD-10-CM coding and documentation guide for Crigler-Najjar Syndrome with Vasculitis. Includes clinical validation requirements, documentation requirements, and coding pitfalls.
Also known as:
Related ICD-10 Code Ranges
Complete code families applicable to Crigler-Najjar Syndrome with Vasculitis
E80.5Primary Range
Disorders of bilirubin metabolism
Primary code for Crigler-Najjar syndrome, a disorder of bilirubin metabolism.
Code Comparison: When to Use Each Code
Compare key differences between these codes to ensure accurate selection
| Code | Description | When to Use | Key Documentation |
|---|---|---|---|
| E80.5 | Crigler-Najjar syndrome | Use when Crigler-Najjar syndrome is confirmed by genetic testing and clinical presentation. |
|
| L95.9 | Vasculitis limited to skin, unspecified | Use when vasculitis is confirmed by biopsy and limited to the skin. |
|
Clinical Decision Support
Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.
Key Information: ICD-10 code for Crigler-Najjar syndrome
Essential facts and insights about Crigler-Najjar Syndrome with Vasculitis
Primary ICD-10-CM Codes for crigler-najjar syndrome vasculitis
Decision Criteria
clinical Criteria
- Presence of UGT1A1 mutation and elevated unconjugated bilirubin.
Applicable To
- Crigler-Najjar type 1
- Crigler-Najjar type 2
Excludes
- Gilbert syndrome (E80.4)
Clinical Validation Requirements
- Genetic testing confirms UGT1A1 mutation
- Unconjugated bilirubin >20 mg/dL
Code-Specific Risks
- Ensure bilirubin levels are documented to avoid misclassification.
Coding Notes
- Ensure genetic testing results are documented for accurate coding.
L95.9 - Vasculitis limited to skin, unspecified
Use when vasculitis is confirmed by biopsy and limited to the skin.
Excludes
- Systemic vasculitis (M31.8)
Clinical Validation Requirements
- Skin biopsy showing leukocytoclastic vasculitis
Coding Notes
Ensure biopsy results are documented to support the code.
Ancillary Codes
Additional codes that should be used in conjunction with the main diagnosis codes when applicable.
Long-term use of phototherapy
Z79.4Documentation & Coding Risks
Avoid these common documentation and coding issues when documenting Crigler-Najjar Syndrome with Vasculitis to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code E80.5.
Impact
Clinical: May lead to misdiagnosis and inappropriate treatment., Regulatory: Non-compliance with coding standards., Financial: Potential for denied claims due to insufficient documentation.
Mitigation Strategy
Ensure biopsy results are included in the patient's record.
Impact
Reimbursement: May lead to incorrect billing and reimbursement issues., Compliance: Non-compliance with coding guidelines., Data Quality: Reduces accuracy of clinical data.
Mitigation Strategy
Omit R17; E80.5 already includes jaundice.
Impact
Coding vasculitis without biopsy confirmation.
Mitigation Strategy
Require biopsy confirmation before coding.
Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.
Frequently Asked Questions
Common questions about ICD-10 coding for Crigler-Najjar Syndrome with Vasculitis, with expert answers to help guide accurate code selection and documentation.
Documentation Templates for Crigler-Najjar Syndrome with Vasculitis
Use these documentation templates to ensure complete and accurate documentation for Crigler-Najjar Syndrome with Vasculitis. These templates include all required elements for proper coding and billing.
Crigler-Najjar syndrome with skin vasculitis
Specialty: PediatricsRequired Elements
- Genetic testing results
- Bilirubin levels
- Biopsy results
Example Documentation
Examples: Poor vs. Good Documentation
Poor Documentation Example
Good Documentation Example
Explanation
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