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ICD-10 Coding for Dandy-Walker Syndrome(Q03.1, O35.0XX1)

Complete ICD-10-CM coding and documentation guide for Dandy-Walker Syndrome. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

Dandy-Walker MalformationDandy-Walker ComplexDandy-Walker Variant

Related ICD-10 Code Ranges

Complete code families applicable to Dandy-Walker Syndrome

Q03.0-Q03.9Primary Range

Congenital Hydrocephalus

Includes codes for hydrocephalus associated with Dandy-Walker malformation.

Maternal care for suspected fetal abnormality and damage

Used for prenatal cases where fetal anomalies are suspected.

Chromosomal anomalies, not elsewhere classified

Used when Dandy-Walker is associated with chromosomal deletions.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
Q03.1Dandy-Walker malformationUse when all three criteria of Dandy-Walker malformation are confirmed via imaging.
  • MRI showing hypoplastic/absent cerebellar vermis
  • Cystic dilation of the fourth ventricle
  • Enlarged posterior fossa
O35.0XX1Maternal care for suspected fetal abnormality and damageUse in prenatal cases where fetal Dandy-Walker is suspected.
  • Prenatal ultrasound or MRI findings indicating CNS anomalies

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for Dandy-Walker syndrome

Essential facts and insights about Dandy-Walker Syndrome

The ICD-10 code for Dandy-Walker syndrome is Q03.1, used when all diagnostic criteria are confirmed via imaging.

Primary ICD-10-CM Codes for dandy walker syndrome

Dandy-Walker malformation
Billable Code

Decision Criteria

clinical Criteria

  • Presence of all three diagnostic criteria on imaging

Applicable To

  • Hydrocephalus with Dandy-Walker malformation

Excludes

  • Q03.8 (Other congenital hydrocephalus)

Clinical Validation Requirements

  • MRI showing hypoplastic/absent cerebellar vermis
  • Cystic dilation of the fourth ventricle
  • Enlarged posterior fossa

Code-Specific Risks

  • Misclassification as unspecified hydrocephalus (Q03.9)

Coding Notes

  • Ensure all three diagnostic criteria are documented to avoid misclassification.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Ventricular septal defect

Q21.0
Use when a cardiac defect is present alongside Dandy-Walker.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Congenital hydrocephalus, unspecified

Q03.9
Use when specific features of Dandy-Walker are not documented.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Dandy-Walker Syndrome to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code Q03.1.

Impact

Clinical: Potential misdiagnosis or delayed treatment., Regulatory: Non-compliance with coding guidelines., Financial: Reduced reimbursement due to lack of specificity.

Mitigation Strategy

Require detailed imaging reports for all suspected cases.

Impact

Reimbursement: Lower reimbursement due to unspecified coding., Compliance: Non-compliance with specificity requirements., Data Quality: Decreased data accuracy for clinical research.

Mitigation Strategy

Use Q03.1 when Dandy-Walker criteria are met.

Impact

Risk of using unspecified codes when specific criteria are met.

Mitigation Strategy

Educate coders on the specific criteria for Dandy-Walker malformation.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Dandy-Walker Syndrome, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Dandy-Walker Syndrome

Use these documentation templates to ensure complete and accurate documentation for Dandy-Walker Syndrome. These templates include all required elements for proper coding and billing.

Neonatal diagnosis of Dandy-Walker

Specialty: Pediatrics

Required Elements

  • Imaging findings
  • Genetic test results
  • Developmental assessments

Example Documentation

MRI confirms Dandy-Walker malformation with complete vermian agenesis and cystic dilation.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Cerebellar abnormalities noted.
Good Documentation Example
MRI confirms Dandy-Walker malformation with complete vermian agenesis, cystic dilation of the fourth ventricle, and enlarged posterior fossa.
Explanation
The good example provides specific imaging findings that confirm the diagnosis.

Need help with ICD-10 coding for Dandy-Walker Syndrome? Ask your questions below.

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