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ICD-10 Coding for Granulomatosis with Polyangiitis(M31.30, M31.31)

Complete ICD-10-CM coding and documentation guide for Granulomatosis with Polyangiitis. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

Wegener's GranulomatosisGPA

Related ICD-10 Code Ranges

Complete code families applicable to Granulomatosis with Polyangiitis

M30-M36Primary Range

Systemic connective tissue disorders

This range includes codes for systemic vasculitides, including granulomatosis with polyangiitis.

Pyogenic granuloma

This code is for pyogenic granuloma, which is a different condition and should not be confused with GPA.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
M31.30Wegener's granulomatosis without renal involvementUse when GPA is diagnosed without renal involvement.
  • Necrotizing granulomas on biopsy
  • PR3-ANCA positivity
M31.31Wegener's granulomatosis with renal involvementUse when GPA is diagnosed with renal involvement.
  • Necrotizing granulomas on biopsy
  • PR3-ANCA positivity
  • Renal biopsy showing glomerulonephritis

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for granulomatosis

Essential facts and insights about Granulomatosis with Polyangiitis

The ICD-10 code for granulomatosis with polyangiitis without renal involvement is M31.30, and with renal involvement is M31.31.

Primary ICD-10-CM Codes for granulomatosis

Wegener's granulomatosis without renal involvement
Billable Code

Decision Criteria

clinical Criteria

  • No renal involvement confirmed by clinical assessment.

Applicable To

  • Granulomatosis with polyangiitis without renal involvement

Excludes

  • M31.31 (with renal involvement)

Clinical Validation Requirements

  • Necrotizing granulomas on biopsy
  • PR3-ANCA positivity

Code-Specific Risks

  • Incorrectly coding when renal involvement is present.

Coding Notes

  • Ensure documentation specifies absence of renal involvement.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Hemoptysis

R04.2
Use to document hemoptysis as a symptom of GPA.

Chronic kidney disease, unspecified

N18.9
Use to document renal involvement in GPA.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Wegener's granulomatosis with renal involvement

M31.31
Presence of renal involvement such as glomerulonephritis.

Wegener's granulomatosis without renal involvement

M31.30
Absence of renal involvement.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Granulomatosis with Polyangiitis to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code M31.30.

Impact

Clinical: May lead to misdiagnosis or incorrect treatment., Regulatory: Non-compliance with documentation standards., Financial: Potential for claim denials.

Mitigation Strategy

Ensure ANCA results are included in all relevant documentation.

Impact

Reimbursement: Incorrect coding can lead to reduced reimbursement., Compliance: Non-compliance with coding guidelines., Data Quality: Inaccurate clinical data affecting patient records.

Mitigation Strategy

Ensure documentation clearly states whether renal involvement is present.

Impact

Lack of ANCA test documentation can trigger audits.

Mitigation Strategy

Ensure all ANCA test results are documented.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Granulomatosis with Polyangiitis, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Granulomatosis with Polyangiitis

Use these documentation templates to ensure complete and accurate documentation for Granulomatosis with Polyangiitis. These templates include all required elements for proper coding and billing.

GPA with renal involvement

Specialty: Rheumatology

Required Elements

  • Biopsy findings
  • ANCA test results
  • Renal function tests

Examples: Poor vs. Good Documentation

Poor Documentation Example
Patient has vasculitis.
Good Documentation Example
Patient diagnosed with GPA confirmed by biopsy showing necrotizing granulomas and PR3-ANCA positivity. Renal biopsy indicates glomerulonephritis.
Explanation
The good example provides specific diagnostic details and test results.

Need help with ICD-10 coding for Granulomatosis with Polyangiitis? Ask your questions below.

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