ICD-10 Coding for Marfan Syndrome(Q87.410, Q87.40)
Complete ICD-10-CM coding and documentation guide for Marfan Syndrome. Includes clinical validation requirements, documentation requirements, and coding pitfalls.
Also known as:
Related ICD-10 Code Ranges
Complete code families applicable to Marfan Syndrome
Q87.4Primary Range
Congenital malformation syndromes predominantly associated with short stature
This range includes codes specifically for Marfan syndrome and its manifestations.
Code Comparison: When to Use Each Code
Compare key differences between these codes to ensure accurate selection
| Code | Description | When to Use | Key Documentation |
|---|---|---|---|
| Q87.410 | Marfan syndrome with aortic dilation | Use when Marfan syndrome is confirmed with documented aortic dilation. |
|
| Q87.40 | Marfan syndrome, unspecified | Use when Marfan syndrome is documented without specific mention of aortic dilation. |
|
Clinical Decision Support
Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.
Key Information: ICD-10 code for Marfan syndrome with aortic dilation
Essential facts and insights about Marfan Syndrome
Primary ICD-10-CM Codes for marfan syndrome
Decision Criteria
clinical Criteria
- Presence of aortic dilation confirmed by echocardiogram
documentation Criteria
- Documentation must explicitly state 'aortic dilation'
Applicable To
- Marfan syndrome with aortic root dilation
Excludes
- Loeys-Dietz syndrome
Clinical Validation Requirements
- Echocardiogram showing aortic root diameter ≥4.5 cm
- Genetic testing confirming FBN1 mutation
Code-Specific Risks
- Incorrectly coding without aortic dilation documentation
Coding Notes
- Ensure documentation specifies aortic involvement to use Q87.410.
Q87.40 - Marfan syndrome, unspecified
Use when Marfan syndrome is documented without specific mention of aortic dilation.
Applicable To
- Marfan syndrome without specified aortic involvement
Excludes
- Loeys-Dietz syndrome
Clinical Validation Requirements
- Clinical diagnosis of Marfan syndrome without specific cardiovascular findings
Coding Notes
Use this code when no specific cardiovascular manifestations are documented.
Ancillary Codes
Additional codes that should be used in conjunction with the main diagnosis codes when applicable.
Thoracic aortic aneurysm
I71.2Differential Codes
Alternative codes to consider when ruling out similar conditions to the primary diagnosis.
Documentation & Coding Risks
Avoid these common documentation and coding issues when documenting Marfan Syndrome to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code Q87.410.
Impact
Clinical: Inaccurate clinical picture of the patient's condition., Regulatory: Potential for audit discrepancies., Financial: Loss of appropriate reimbursement.
Mitigation Strategy
Regular training on documentation standards, Use of templates that prompt for specific measurements
Impact
Reimbursement: Incorrect coding may lead to underpayment., Compliance: Non-compliance with coding guidelines., Data Quality: Inaccurate clinical data representation.
Mitigation Strategy
Ensure documentation specifies aortic dilation if present to use Q87.410.
Impact
Risk of audits due to insufficient documentation of aortic involvement in Marfan syndrome.
Mitigation Strategy
Ensure echocardiogram results are consistently documented.
Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.
Frequently Asked Questions
Common questions about ICD-10 coding for Marfan Syndrome, with expert answers to help guide accurate code selection and documentation.
Documentation Templates for Marfan Syndrome
Use these documentation templates to ensure complete and accurate documentation for Marfan Syndrome. These templates include all required elements for proper coding and billing.
Cardiology follow-up for Marfan syndrome
Specialty: CardiologyRequired Elements
- Patient demographics
- Genetic testing results
- Echocardiogram findings
- Family history
Example Documentation
Examples: Poor vs. Good Documentation
Poor Documentation Example
Good Documentation Example
Explanation
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