Back to HomeBeta

ICD-10 Coding for Neuromyelitis Optica(G36.0)

Complete ICD-10-CM coding and documentation guide for Neuromyelitis Optica. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

Devic's DiseaseNMONeuromyelitis Optica Spectrum Disorder

Related ICD-10 Code Ranges

Complete code families applicable to Neuromyelitis Optica

G35-G37Primary Range

Demyelinating diseases of the central nervous system

This range includes codes for demyelinating diseases, with G36.0 specifically for neuromyelitis optica.

Key Information: ICD-10 code for neuromyelitis optica

Essential facts and insights about Neuromyelitis Optica

The ICD-10 code for neuromyelitis optica is G36.0, used for confirmed NMOSD cases with AQP4-IgG positivity.

Primary ICD-10-CM Code for neuromyelitis optica

Neuromyelitis optica [Devic]
Billable Code

Decision Criteria

clinical Criteria

  • Presence of AQP4-IgG antibodies and LETM on MRI

Applicable To

  • Neuromyelitis optica spectrum disorder

Excludes

  • Optic neuritis (H46)

Clinical Validation Requirements

  • AQP4-IgG positivity
  • Longitudinally extensive transverse myelitis (LETM)
  • Optic neuritis

Code-Specific Risks

  • Confusion with multiple sclerosis
  • Incorrect use of optic neuritis code

Coding Notes

  • Ensure documentation includes AQP4-IgG status and MRI findings.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Injection, inebilizumab-cdon, 1 mg

J1823
Use for inebilizumab administration in NMOSD treatment.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Unspecified optic neuritis

H46.9
Use H46.9 for isolated optic neuritis without NMOSD criteria.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Neuromyelitis Optica to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code G36.0.

Impact

Clinical: Inaccurate diagnosis and treatment planning., Regulatory: Non-compliance with documentation standards., Financial: Potential claim denials due to insufficient documentation.

Mitigation Strategy

Ensure MRI reports are included in patient records, Verify documentation before claim submission

Impact

Reimbursement: Incorrect coding may lead to denied claims., Compliance: Non-compliance with ICD-10 guidelines., Data Quality: Inaccurate clinical data representation.

Mitigation Strategy

Confirm NMOSD diagnosis with AQP4-IgG and MRI findings before coding.

Impact

Coding NMOSD without documented AQP4-IgG results.

Mitigation Strategy

Require serology documentation before coding.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Neuromyelitis Optica, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Neuromyelitis Optica

Use these documentation templates to ensure complete and accurate documentation for Neuromyelitis Optica. These templates include all required elements for proper coding and billing.

Initial NMOSD diagnosis

Specialty: Neurology

Required Elements

  • Patient history of optic neuritis
  • MRI findings of LETM
  • AQP4-IgG serology results

Example Documentation

Patient presents with bilateral vision loss and MRI shows LETM. AQP4-IgG positive. Diagnosis: NMOSD.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Optic neuritis and myelitis. Rule out MS vs NMO.
Good Documentation Example
48hr history of bilateral vision loss with LETM on MRI and positive AQP4-IgG by CBA. NMOSD diagnosed per 2015 IPND criteria.
Explanation
The good example includes specific diagnostic criteria and test results, confirming NMOSD.

Need help with ICD-10 coding for Neuromyelitis Optica? Ask your questions below.

Ask about any ICD-10 CM code, or paste a medical note

We build tools for
clinician happiness.

Learn More at Freed.ai
Back to HomeBeta

Built by Freed

Try Freed for free for 7 days.

Learn more