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ICD-10 Coding for Pernicious Anemia(D51.0, D51.9)

Complete ICD-10-CM coding and documentation guide for Pernicious Anemia. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

Vitamin B12 Deficiency AnemiaAddisonian Anemiaaddisons anemia

Related ICD-10 Code Ranges

Complete code families applicable to Pernicious Anemia

D50-D53Primary Range

Nutritional anemias

This range includes pernicious anemia and other nutritional anemias.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
D51.0Pernicious anemiaUse when intrinsic factor deficiency is confirmed with lab tests.
  • Positive intrinsic factor antibody
  • Elevated serum gastrin >200 pg/mL
  • Methylmalonic acid >0.4 nmol/mL
D51.9Vitamin B12 deficiency anemia, unspecifiedUse when the cause of B12 deficiency is unclear or not documented.
  • Low serum B12 without intrinsic factor deficiency confirmation

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for pernicious anemia

Essential facts and insights about Pernicious Anemia

The ICD-10 code for pernicious anemia is D51.0, used when intrinsic factor deficiency is confirmed.

Primary ICD-10-CM Codes for pernicious anemia

Pernicious anemia
Billable Code

Decision Criteria

clinical Criteria

  • Positive intrinsic factor antibody test

documentation Criteria

  • Documented intrinsic factor deficiency

Applicable To

  • Autoimmune gastritis with intrinsic factor deficiency

Excludes

  • Vitamin B12 deficiency anemia NOS (D51.9)

Clinical Validation Requirements

  • Positive intrinsic factor antibody
  • Elevated serum gastrin >200 pg/mL
  • Methylmalonic acid >0.4 nmol/mL

Code-Specific Risks

  • Incorrectly coding as D51.9 without confirming intrinsic factor deficiency.

Coding Notes

  • Ensure documentation specifies intrinsic factor deficiency.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Anemia in chronic kidney disease

D63.1
Use when CKD is present; code CKD first.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Vitamin B12 deficiency anemia, unspecified

D51.9
Use when intrinsic factor deficiency is not confirmed.

Pernicious anemia

D51.0
Use when intrinsic factor deficiency is confirmed.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Pernicious Anemia to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code D51.0.

Impact

Clinical: Misdiagnosis of anemia type., Regulatory: Non-compliance with coding standards., Financial: Potential for incorrect billing and reimbursement.

Mitigation Strategy

Ensure lab tests are ordered and results documented., Educate providers on documentation standards.

Impact

Reimbursement: Incorrect DRG assignment leading to potential underpayment., Compliance: Non-compliance with coding guidelines., Data Quality: Inaccurate clinical data affecting patient records.

Mitigation Strategy

Ensure documentation includes intrinsic factor antibody test results.

Impact

Using D51.9 instead of D51.0 when intrinsic factor deficiency is confirmed.

Mitigation Strategy

Regular audits and provider education on documentation requirements.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Pernicious Anemia, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Pernicious Anemia

Use these documentation templates to ensure complete and accurate documentation for Pernicious Anemia. These templates include all required elements for proper coding and billing.

Diagnosis of Pernicious Anemia

Specialty: Hematology

Required Elements

  • Symptoms of anemia
  • Lab results: B12, MMA, IFBA
  • Treatment plan

Example Documentation

Patient presents with fatigue and macrocytic anemia. Labs show B12 150 pg/mL, MMA 0.6 nmol/mL, positive IFBA. Plan: B12 injections.

Examples: Poor vs. Good Documentation

Poor Documentation Example
B12 deficiency anemia
Good Documentation Example
Pernicious anemia confirmed by positive IFBA and elevated gastrin.
Explanation
The good example specifies the cause and confirms the diagnosis with lab results.

Need help with ICD-10 coding for Pernicious Anemia? Ask your questions below.

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