Back to HomeBeta

ICD-10 Coding for Polycystic Kidney Disease(Q61.2, Q61.3)

Complete ICD-10-CM coding and documentation guide for Polycystic Kidney Disease. Includes clinical validation requirements, documentation requirements, and coding pitfalls.

Also known as:

PKDAutosomal Dominant Polycystic Kidney DiseaseADPKDAutosomal Recessive Polycystic Kidney DiseaseARPKD

Related ICD-10 Code Ranges

Complete code families applicable to Polycystic Kidney Disease

Q61.0-Q61.9Primary Range

Congenital malformations of the kidney

This range includes all types of polycystic kidney disease, both autosomal dominant and recessive.

Chronic kidney disease (CKD) stages

Used to specify the stage of CKD when associated with PKD.

Hypertensive kidney disease

Used when hypertension is present with CKD due to PKD.

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescriptionWhen to UseKey Documentation
Q61.2Polycystic kidney, adult typeUse for adult patients with confirmed ADPKD.
  • Family history of ADPKD
  • Ultrasound showing ≥3 unilateral cysts (age <40) or ≥2 bilateral cysts (age >40)
Q61.3Polycystic kidney, infantile typeUse for infant patients with confirmed ARPKD.
  • Onset in infancy
  • Hepatic fibrosis on imaging

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information: ICD-10 code for polycystic kidney disease

Essential facts and insights about Polycystic Kidney Disease

The ICD-10 code for autosomal dominant polycystic kidney disease is Q61.2, while Q61.3 is used for autosomal recessive polycystic kidney disease.

Primary ICD-10-CM Codes for polycystic kidney disease

Polycystic kidney, adult type
Billable Code

Decision Criteria

clinical Criteria

  • Presence of multiple renal cysts and family history of ADPKD.

documentation Criteria

  • Documented CKD stage if renal impairment is present.

Applicable To

  • Autosomal Dominant Polycystic Kidney Disease (ADPKD)

Excludes

  • Autosomal Recessive Polycystic Kidney Disease (Q61.3)

Clinical Validation Requirements

  • Family history of ADPKD
  • Ultrasound showing ≥3 unilateral cysts (age <40) or ≥2 bilateral cysts (age >40)

Code-Specific Risks

  • Misclassification with ARPKD in adults

Coding Notes

  • Ensure documentation specifies ADPKD and any associated CKD stage.

Ancillary Codes

Additional codes that should be used in conjunction with the main diagnosis codes when applicable.

Chronic kidney disease stage

N18.x
Use to specify CKD stage when renal impairment is present.

Hypertensive CKD

I12.9
Use when hypertension is documented as causal.

Differential Codes

Alternative codes to consider when ruling out similar conditions to the primary diagnosis.

Polycystic kidney, infantile type

Q61.3
Typically presents in infancy with hepatic fibrosis and consanguinity.

Polycystic kidney, adult type

Q61.2
Typically presents in adulthood with family history.

Documentation & Coding Risks

Avoid these common documentation and coding issues when documenting Polycystic Kidney Disease to ensure proper reimbursement, maintain compliance, and reduce audit risk. These guidelines are particularly important when using ICD-10 code Q61.2.

Impact

Clinical: Inaccurate assessment of disease progression., Regulatory: Non-compliance with coding standards., Financial: Potential for reduced reimbursement.

Mitigation Strategy

Ensure eGFR and CKD stage are documented in every visit.

Impact

Reimbursement: Incorrect coding may lead to denied claims., Compliance: Non-compliance with coding guidelines., Data Quality: Inaccurate patient records and statistics.

Mitigation Strategy

Ensure age and clinical presentation match ARPKD criteria.

Impact

Failure to document CKD stage can lead to audit issues.

Mitigation Strategy

Implement checklist for CKD documentation.

Documentation errors, coding pitfalls, and audit risks are interconnected aspects of medical coding and billing. Addressing all three areas helps ensure accurate coding, optimal reimbursement, and regulatory compliance.

Frequently Asked Questions

Common questions about ICD-10 coding for Polycystic Kidney Disease, with expert answers to help guide accurate code selection and documentation.

Documentation Templates for Polycystic Kidney Disease

Use these documentation templates to ensure complete and accurate documentation for Polycystic Kidney Disease. These templates include all required elements for proper coding and billing.

Nephrology Consultation

Specialty: Nephrology

Required Elements

  • Family history
  • Imaging results
  • CKD stage

Example Documentation

Patient presents with ADPKD confirmed by ultrasound showing multiple cysts. Family history positive for PKD in father. CKD stage 3b with eGFR 45 mL/min.

Examples: Poor vs. Good Documentation

Poor Documentation Example
Patient has kidney cysts.
Good Documentation Example
ADPKD confirmed by abdominal CT showing bilateral >10 cysts per kidney, family history of PKD in father.
Explanation
The good example provides specific imaging findings and family history, which are necessary for accurate coding.

Need help with ICD-10 coding for Polycystic Kidney Disease? Ask your questions below.

Ask about any ICD-10 CM code, or paste a medical note

We build tools for
clinician happiness.

Learn More at Freed.ai
Back to HomeBeta

Built by Freed

Try Freed for free for 7 days.

Learn more